The familial complete atrioventricular block, is an inherited disease, may appear in adult period [1–3]. A 39-year-oldwoman had symptomatic (two episodes of near syncope during exertion) complete atrioventricular block (QRS wave ≤0,12 second on the surface electrocardiography) (Fig. 1) and was successfully treated with permanent dual chamber (DDDR) pacemakers. Her father, a 66-year-old-, had also complete atrioventricular block who was successfully treated with DDDR pacemaker in the another hospital about 7 years ago. Her other family members had normal sinus rhythm. She and her father had not any disease such as hypertension, diabetes mellitus, rhumatologic disease and valvular heart disease. Their laboratory tests such as complete blood count, urea, creatinine, potassium, magnesium, thyroid function tests, antinuclear antibody, romatoid factor and transthoracic echocardiogram were normal